Dados do Trabalho

Título

Primary intracardiac burkitt's lymphoma in a tennager: case report and review of literature

Apresentação do caso

In May 2023, a 13-year-old male with a previous history of blunt trauma to the chest was evaluated
for a non-obstructive pericardial effusion. A diagnostic pericardial puncture was performed which
showed an increased ADA. The patient had a positive epidemiology for tuberculosis, and it was
decided to start treatment accordingly. Monthly echocardiograms were performed, and, in November
2023, a routine examination showed an image in the right atrium suggestive of a local thrombus. A
subsequent magnetic resonance imaging confirmed the presence of an intracardiac mass. The patient
rapidly evolved with obstructive shock and was placed on ECMO. A biopsy of the lesion revealed
Burkitt Lymphoma. There was no good response to isolated dexamethasone, and it was decided to
add vincristine and cyclophosphamide to cytoreduction. This led to the clearance of the right cardiac
cavities within 48 hours and cardiogenic shock. The patient has been treated with institutional
Non-Hodgkin’s Lymphoma protocol since then with good evolution.

Discussão

Intracardiac lymphomas are rare in pediatrics, and primary cardiac Burkitt Lymphomas are even more
uncommon. Due to its predisposition to rapid growth and high risk of early death, this pathology
should be suspected in cases of intracardiac tumors.

Comentários Finais

Intracardiac Burkitt Lymphomas are rare. A literature review using the terms "Burkitt" and "cardiac"
showed only 28 cases reported between 1975-2023. Among the patients, only 9 were part of the
pediatric population. This report seeks to complement the current literature by describing the case of
a 13-year-old teenager with Intracardiac Burkitt Lymphoma.